I see a lot of people commenting on the short life span for people with CF so I wanted to share this as some encouragement. One of my buddies has CF and is a double lung transplant recipient. He's now an Ironman Triathlete. His story was featured in the book You Are An Ironman, here's an interview with him on the Today show.
I know Scott's story is atypical but what an amazing story he has. Best of luck to you in your battle with CF.